Acta Medica Iranica 2018. 56(8):544-546.

Cytomegalovirus Infection in a Patient With Leukocyte Adhesion Deficiency Type 1
Ahmad Bahrami, Mahnaz Sadeghian, Mehrdad Sheikhvatan, Arash Foroudi, Sara Harsini, Nima Rezaei

Abstract


Leukocyte adhesion deficiency type 1 (LAD-1) is a rare autosomal recessive immunodeficiency disorder, characterized by recurrent bacterial and fungal infections without pus formation. Herein, we report a case of LAD-1 that developed into gastrointestinal cytomegalovirus (CMV) disease and manifested with persistent abdominal pain and bloody diarrhea. Although the presence of concurrent gastrointestinal CMV infection with LAD-1 is a rare condition, this case highlights the need for further research to evaluate the complex mechanisms between LAD-1 and CMV occurrence.


Keywords


Cytomegalovirus; Leukocyte adhesion deficiency type 1; Gastrointestinal tract; Children

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References


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