Tehran University of Medical Sciences Acta Medica Iranica 0044-6025 33 1-2 1995 06 15 35 38 Mostafa Mirshams-Shahshahani Zahra Safaii-Naraghi   Mohammad-Reza Mortazavi 2015 09 28 The present study introduces a rare case of phakomatosispigmenJovascularis, which is charaderiud by the existence ofpigmentary naevus ond vascular naevus. Until 1985, 63 cases ofthis syndrome have been reported, mostly in Japon (56 cases). This is the first case of phakomatosis pigmentovascularis, reported in Iran. https://acta.tums.ac.ir/index.php/acta/article/view/1661 https://acta.tums.ac.ir/index.php/acta/article/download/1661/1654