Tehran University of Medical Sciences Acta Medica Iranica 0044-6025 44 1 2006 02 15 59 62 G. Iravanlo Z. Nozarian 2015 09 28 Perivascular epithelioid cell tumor (PEComa) is composed of HMB45+ epithelioid cells with clear to granular cytoplasm and perivascular distribution. We describe a uterine PEComa in a 33 years old woman where tumor cells were positive for HMB45 but negative for epithelial markers and negative or positive for smooth muscles markers. https://acta.tums.ac.ir/index.php/acta/article/view/3141 https://acta.tums.ac.ir/index.php/acta/article/download/3141/3121