Tehran University of Medical Sciences Acta Medica Iranica 0044-6025 55 7 2017 09 16 470 473 EN Fariba Abbasi Department of Pathology, Solid Tumor Research Center, Urmia University of Medical Sciences, Urmia, Iran. Ata Abbasi Department of Pathology, School of Medicine, Urmia University of Medical Sciences, Urmia, Iran. Mansour Alizadeh Department of Urology, Urmia Urology and Nephrology Research Center, Urmia University of Medical Sciences, Urmia, Iran. Parisa Modarresi Department of Pathology, School of Medicine, Urmia University of Medical Sciences, Urmia, Iran. 2015 11 14 2016 10 14 Angiomyolipoma (AML) and oncocytoma are uncommon benign neoplasms of the kidney which their simultaneous occurrence in the same kidney is extremely rare. This study reports a 60-year-old diabetic woman with the rare simultaneous occurrence of three renal masses. Histologic evaluation revealed two angiomyolipomas and one oncocytoma within the same kidney, in a background of histologic features of diabetic nephropathy. Renal angiomyolipoma and oncocytoma are uncommon neoplasms, and their simultaneous occurrence in the same kidney is extremely rare. https://acta.tums.ac.ir/index.php/acta/article/view/5140 https://acta.tums.ac.ir/index.php/acta/article/download/5140/4966