Tehran University of Medical Sciences Acta Medica Iranica 0044-6025 54 1 2016 02 01 72 75 EN Hamid Ahmadi Department of General Surgery, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran. Mahdieh Mohammad Khan Tehrani Department of General Surgery, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran. 2016 01 20 Wandering spleen is an uncommon entity in adults and has been described only rarely with sigmoid volvulus, that rarely affects children and adolescents. It is usually described in adults.Wandering spleen characterized by the abnormal location of the spleen, caused by incomplete fusion of the four primary splenic ligaments, allowing the spleen to be mobile within the abdomen.The wandering spleen can lead to torsion and subsequent splenic infarction or rupture. Clinical suspicion plus urgent investigation and intervention are important. We present a rare clinical case of acute abdomen due to torsion of wandering spleen and volvulus of sigmoid in a 14-year-old girl presented with painful periumbilical mass. Detorsion of sigmoid occurred while undergoing exploratory laparotomy and splenectomy was performed. The possibility of torsion and its complication like gastric, pancreas tail and colon volvulus should be kept in mind in the differential diagnosis of the acute abdomen to avoid serious complications. https://acta.tums.ac.ir/index.php/acta/article/view/5392 https://acta.tums.ac.ir/index.php/acta/article/download/5392/4741