“Eye of the Tiger” in a Non-Responsive Neuropsychiatric Patient: A Case Report

  • Milad Hosseinialhashemi Student's Research Committee, Shiraz University of Medical Sciences, Shiraz, Iran.
  • Babak Daneshfard Research Center for Traditional Medicine and History of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran. AND Essence of Parsiyan Wisdom Institute, Phytopharmaceutical Technology and Traditional Medicine Incubator, Shiraz University of Medical Sciences, Shiraz, Iran. AND Department of Persian Medicine, School of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran.
  • Atefe Hashemi Student's Research Committee, Shiraz University of Medical Sciences, Shiraz, Iran.
Keywords: Pantothenate kinase-associated neurodegeneration, Hallervorden-Spatz syndrome, Neurodegenerative diseases, Magnetic resonance imaging, Case report

Abstract

Hallervorden-Spatz syndrome is a rare neurodegenerative disorder with hereditary properties. It usually occurs in young adolescents with extrapyramidal symptoms besides disturbed mental function. In this study, we present a 23-year-old neuropsychiatric patient who primarily misdiagnosed to have conversion disorder. She had 5-year history of progressive dysarthria and generalized abnormal movements. After detecting the pathognomonic sign of “eye of the tiger” diagnosis was confirmed. The patient was discharged. She had satisfactory condition in her follow-up. Such a rare syndrome should be considered in patients with similar presentation, and upon the diagnosis, PKAN2 gene study should be done to detect possible new mutations.     

References

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Published
2018-02-05
How to Cite
1.
Hosseinialhashemi M, Daneshfard B, Hashemi A. “Eye of the Tiger” in a Non-Responsive Neuropsychiatric Patient: A Case Report. Acta Med Iran. 56(1):71-3.
Section
Case Report(s)