Histiocytic Sarcoma of Nasal Cavity: A Case Report

  • Flavia Watusi Faria Pediatric Oncologist, Children’s Hospital of Brasília José Alencar, Brasília-DF, Brazil.
  • Vitorino Modesto dos Santos Department of Internal Medicine, Armed Forces Hospital and Catholic University of Brasília, Brasília-DF, Brazil.
  • Lara Vieira da Silva Meira Department of Internal Medicine, Ex-Intern, Catholic University of Brasília, Brasília-DF, Brazil.
Keywords: Nasal cavity, Immunohistochemistry, Chemotherapy, Histiocytic sarcoma

Abstract

Histiocytic sarcoma is a rare hematopoietic malignancy that originates from histiocytes, and may involve lymph nodes and extranodal sites such as the spleen, head and neck, skeleton, liver, breast, bone marrow, mediastinum, pancreas, skin, lung, kidney, central nervous system, testis, gastrointestinal tract, and uterus. The involvement of the nasal cavity is considered extremely rare. The prognosis is poor, even with chemotherapy, and the survival time is usually two years. We report the case of a 16-year-old-male with primary histiocytic sarcoma of the nasal cavity. The diagnosis was based on classical histopathology and immunohistochemical findings. This malignancy has not shown consistent satisfactory responses to chemotherapy regimens.

Author Biographies

Flavia Watusi Faria, Pediatric Oncologist, Children’s Hospital of Brasília José Alencar, Brasília-DF, Brazil.

Pediatric Oncologist

Vitorino Modesto dos Santos, Department of Internal Medicine, Armed Forces Hospital and Catholic University of Brasília, Brasília-DF, Brazil.

Adjunct-Professor of the Internal Medicine Department

Lara Vieira da Silva Meira, Department of Internal Medicine, Ex-Intern, Catholic University of Brasília, Brasília-DF, Brazil.

Medical Doctor, Internal Medicine

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Published
2019-01-16
How to Cite
1.
Faria F, Modesto dos Santos V, Vieira da Silva Meira L. Histiocytic Sarcoma of Nasal Cavity: A Case Report. Acta Med Iran. 56(11):726-728.
Section
Case Report(s)