Primary Peritoneal Hydatidosis Mimicking Pseudomyxoma Peritonei: A Case Report
Abstract
Primary peritoneal hydatidosis is a rare form of cystic echinococcosis characterized by peritoneal involvement without prior hepatic or pulmonary disease. This condition may present with non-specific symptoms such as abdominal pain or distention and is frequently misdiagnosed due to its radiologic similarity to other intra-abdominal cystic pathologies. In this report, we describe a 37-year-old man with no relevant past medical history who presented with diffuse intra-abdominal cystic lesions initially suggestive of pseudomyxoma peritonei. Imaging, particularly computed tomography, revealed numerous non-enhancing cystic lesions throughout the peritoneal cavity, raising the suspicion of disseminated cystic disease. Surgical exploration and histopathological examination confirmed the diagnosis of primary peritoneal hydatidosis. This case underscores the importance of considering hydatid disease in the differential diagnosis, particularly in endemic regions.
2. Wani RA, Wani I, Malik AA, Parray FQ, Wani AA, Dar AM. Hydatid disease at unusual sites. Int J Case Rep Images. 2012;3(6):1-6.
3. Yuksel M, Demirpolat G, Sever A, Bakaris S, Bulbuloglu E, Elmas N. Hydatid disease involving some rare locations in the body: a pictorial essay. Korean journal of radiology. 2007;8(6):531-40.
4. Pedrosa I, Saíz A, Arrazola J, Ferreirós J, Pedrosa CS. Hydatid Disease: Radiologic and Pathologic Features and Complications. RadioGraphics. 2000;20(3):795-817.
5. Kosmidis C, Efthimiadis C, Anthimidis G, Vasileiadou K, Koimtzis G, Tzeveleki I, et al. Management of peritoneal hydatid cysts: A fourty-year experience. Heliyon. 2018;4(12):e00994.
6. Das CJ, Venkatesh SSK, Gupta S, Sharma R, Agarwal D, Kundra V. Abdominal hydatid disease: role of imaging in diagnosis, complications, and management. Abdominal radiology (New York). 2025.
7. Polat P, Kantarci M, Alper F, Suma S, Koruyucu MB, Okur A. Hydatid disease from head to toe. Radiographics. 2003;23(2):475-94; quiz 536-7.
8. Balik AA, Celebi F, Başglu M, Oren D, Yildirgan I, Atamanalp SS. Intra-abdominal extrahepatic echinococcosis. Surgery today. 2001;31(10):881-4.
9. Gourgiotis S, Stratopoulos C, Moustafellos P, Dimopoulos N, Papaxoinis G, Vougas V, et al. Surgical techniques and treatment for hepatic hydatid cysts. Surgery today. 2007;37(5):389-95.
10. Karavias DD, Vagianos CE, Kakkos SK, Panagopoulos CM, Androulakis JA. Peritoneal echinococcosis. World journal of surgery. 1996;20(3):337-40.
11. Kushwaha JK, Sonkar AA, Verma AK, Pandey SK. Primary disseminated extrahepatic abdominal hydatid cyst: a rare disease. BMJ case reports. 2012;2012.
12. Sarkar D, Ray S, Saha M. Peritoneal hydatidosis: A rare form of a common disease. Tropical parasitology. 2011;1(2):123-5.
13. Astarcioglu H, Koçdor MA, Topalak O, Terzi C, Sökmen S, Ozer E. Isolated mesosigmoidal hydatid cyst as an unusual cause of colonic obstruction: report of a case. Surgery today. 2001;31(10):920-2.
14. Hegde N, Hiremath B. Primary peritoneal hydatidosis. BMJ case reports. 2013;2013:bcr2013200435.
15. Babu KS, Goel D, Prayaga A, Rao IS, Kumar A. Intraabdominal hydatid cyst: a case report. Acta cytologica. 2008;52(4):464-6.
16. De U. Primary abdominal hydatid cyst presenting in emergency as appendicular mass: a case report. World journal of emergency surgery : WJES. 2009;4:13.
17. Rosales-Castañeda E, Martínez-Ordaz JL, Estrada-Castellanos A, Goméz-Jiménez LM. [Disseminated peritoneal hydatidosis manifested as intestinal ischaemia]. Cirugia y cirujanos. 2017;85(3):269-72.
| Files | ||
| Issue | Articles in Press: Vol 64 No 02 (2026) | |
| Section | Case Report(s) | |
| Keywords | ||
| Echinococcus granulosus Hydatidosis Hydatid Cyst | ||
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