"A research on Hirschsprung’s disease in Amirkabir and Bahrami children hospitals "

Abstract

Hirchsprung’s disease is a developmental disorder of the enteric nervous system, characterized by abdsence of ganglion cell in the myenterric and submucosal plexuese along a variable portion of the distal intestine.The purpose of this study is the presentation of a new procedure for reduction of the postoperative complications of Hirschsprung’s disease (HD) by offering a modified Swenson’s technique. This was a chieved through a 10 years study of 157 patients with HD, of whom 74% were male and 26% wre female. In 100 cases the disease was diagnosed in the early neonatal period, in 129 cases the involved segments were rectosigmoid or shortsegment. Our choice of operation was a new modification of swenson’s type of pull through (Swenson’s operation + posterior rectal wall myectomy). Phatholgical examination has confirmed the diagnosis of HD in all patients. The overall results of surgery were good in 81% and there was no mortality.