Simultaneous Shoulder and Hip Dislocation in a 12-Year-Old Girl with Hutchinson-Gilford Progeria Syndrome

  • Ramin Espandar Department of Orthopedic, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran.
  • Amir Sobhani Eraghi Department of Orthopedic, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran.
  • Shirin Mardookhpour Department of Radiology, Tehran University of Medical sciences, Tehran, Iran.
Keywords:
Accelerated aging, Hutchinson-Gilford progeria syndrome

Abstract

Hutchinson-Gilford progeria syndrome (HGPS) is a rare premature ageing disorder that is characterized by accelerated degenerative changes of the cutaneous, musculoskeletal and cardiovascular systems. Mean age at diagnosis is 2.9 years and generally leading to death at approximately 13 years of age due to myocardial infarction or stroke. Orthopedic manifestations of HGPS are multiple and shoulder dislocation is a rare skeletal trauma in progeria syndrome. Our patient had simultaneous shoulder and hip dislocation associated with a low energy trauma. This subject has not been reported. Treatment accomplished as close reduction under general anesthesia and immobilization.

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How to Cite
1.
Espandar R, Sobhani Eraghi A, Mardookhpour S. Simultaneous Shoulder and Hip Dislocation in a 12-Year-Old Girl with Hutchinson-Gilford Progeria Syndrome. Acta Med Iran. 50(6):439-443.
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