Epidermal Nevus Syndrome and Dysplatic Kidney Disease

  • Azar Nickavar Mail Department of Pediatric Nephrology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.
  • Najmessadat Atefi Department of Dermatology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.
  • Kambiz Kamyab Hesari Department of Pathology, Razi Dermatology Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Keywords:
Epidermal nevus syndrome, Multicystic dysplastic kidney, Wilms' tumor, Neurocutaneous

Abstract

Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.

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How to Cite
1.
Nickavar A, Atefi N, Kamyab Hesari K. Epidermal Nevus Syndrome and Dysplatic Kidney Disease. Acta Med Iran. 52(8):647-649.
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