Orbital Tumor Revealing a Systemic Sarcoidosis

  • Samia Hannanachi Sassi Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
  • Rim Dhouib Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
  • Fatma Kanchal Mail Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
  • Raoudha Doghri Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
  • Nadia Boujelbene Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
  • Hedi Bouguila Department of Ophthalmology, Hedi Rais Institute of Ophthalmology, Bab Saadoun, 1006 Tunis, Tunisia.
  • Karima Mrad Department of Pathology, Salah Azaeiz Institute, Bab Saadoun, 1006 Tunis, Tunisia.
Keywords:
Orbital pseudotumor, Inflammation, Sarcoidosis

Abstract

Ocular involvement is seen in approximately 25% of patients with sarcoidosis. Uveitis is the most common ocular manifestation, but sarcoidosis may involve any part of the eye. Orbital manifestations of sarcoidosis are uncommon with few series in the literature. A 65-year-old woman presented with redness of the right eye and painless, unilateral eyelid swelling. Orbital scanning revealed mass infiltrating the soft tissue of the inferior right orbital quadrant. Biopsy results showed nodular, noncaseating granulomas consistent with sarcoidosis. The complete systemic workup revealed systemic manifestations of sarcoidosis at the time of examination with hilar and mediastinal lymphadenopathies noted on CT scan. The orbital surgical treatment was followed by systemic prednisone therapy with good response. Although rare, orbital sarcoidosis must be considered in the evaluation of orbital tumors in elderly patients. A search for systemic findings should be undertaken and appropriate therapy should be instituted.

References

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How to Cite
1.
Hannanachi Sassi S, Dhouib R, Kanchal F, Doghri R, Boujelbene N, Bouguila H, Mrad K. Orbital Tumor Revealing a Systemic Sarcoidosis. Acta Med Iran. 53(3):195-197.
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