Eosinophilic Granuloma of the Skull Base: Patient with Unique Clinical Moreover, Radiographic Presentation

  • Hosein Dalili Department of Pediatrics, Breast Feeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Zahra Dalili Kajan Mail Department of Maxillofacial Radiology, School of Dentistry, Guilan University of Medical Sciences, Guilan, Iran.
Keywords:
Skull base neoplasm, Cone beam, computed tomography, Temporomandibular, joint disorder

Abstract

This case report presents an eight-year-old girl having periauricular swelling and severe pain during mouth opening on the right-side temporomandibular joint (TMJ). CBCT showed extensive destruction of the base of the skull and the roof of the glenoid fossa on the right side. The findings based on CT and MRI images with and without contrast are discussed herein. This report highlights a skull base eosinophilic granuloma that mimics TMJ disorder and the importance of proper evaluation of CBCT images to make an early diagnosis.

References

D’Ambrosio N, Soohoo S, Warshall C, et al. Craniofacial and intracranial manifestations of Langerhans cell histiocytosis: report of findings in 100 patients. AJR Am J Roentgenol 2008;191(2):589-97.

Nicholson CM, Egeker RM, Nesbit ME. The epidemiology of Langerhans cell histiocytosis. Hematol Oncol Clin North Am 1998;12(2):379-84.

Harris GJ, Woo KI. Eosinophilic granuloma of the orbit: a paradox of aggressive destruction responsive to minimal intervention. Trans Am Ophthalmol Soc 2003;101:93-103.

Egeler RM, Annels NE, Hogendoorn PC. Langerhans cell histiocytosis: a pathologic combination of oncogenesis and immune dysregulation. Pediatr Blood Cancer 2004;42(5): 401-3.

Nelson BL. Langerhans cell histiocytosis of the temporal bone. Head and Neck Pathol 2008;2(2):97-8.

Kasper EM, Aguirre-Padilla DH, Alter RY, et al. characteristics, behavior, and treatments as illustrated in a case series. Surg Neurol Int 2011;2(1):57.

Meyer A, Stark M, Karstens JH, et al. Langerhans cell histiocytosis of the cranial base: is low-dose radiotherapy effective? Case Rep Oncol Med 2012;2012:789640.

Binning MJ, Brockmeyer DL. Novel multidisciplinary approach for the treatment of Langerhans cell histiocytosis of the skull base. Skull Base 2008;18(1):53-8.

Boston M, Derkay CS. Langerhans’ cell histiocytosis of the temporal bone and skull base. Am J Otolaryngol 2002;23(4):246-8.

Khanna G, Sato Y, Smith RJ, et al. Causes of facial swelling in pediatric patients: correlation of clinical and radiologic findings. Radiographics 2006;26(1):157-71.

Gunny R, Clifton A, Al-Memar A. Spontaneous regression of supratentorial intracerebral Langerhans’ cell histiocytosis. Br J Radiol 2004;77(920):685-7.

Greenberger JS, Cassady JR, Jaffe N. Radiation therapy in patients with histiocytosis: management of diabetes insipidus and bone lesions. Int J Radiat Oncol Biol Phys 1979;5(10):1749-55.

Imamura T, Sato T, Shiota Y, et al. Outcome of pediatric patients with Langerhans cell histiocytosis treated with 2 chlorodeoxyadenosine: A nationwide survey in Japan. Int J Hematol 2010;91(4):646-51.

Olschewski T, Seegenschmiedt MH. Radiotherapy for bony manifestations of langerhans cell histiocytosis: review and proposal for an international registry. Strahlenther Onkol 2006;182(2):72-9.

Heyd R, Strassmann G , Donnerstag F, et al. Radiotherapy in Langerhans-cell histiocytosis. 2case reports and review of the literature. Rontgenpraxis 2000;53(2):51-61.

Surico G, Muggeo P, Muggeo V, et al. Ear involvement in childhood Langerhans’ cell histiocytosis. Head Neck 2000;22(1):42-7.

Escardo-Paton JA, Neal J, Lane CM. Late recurrence of Langerhans cell histiocytosis in the orbit. Br J Ophthalmol 2004;88(6):838-9.

How to Cite
1.
Dalili H, Dalili Kajan Z. Eosinophilic Granuloma of the Skull Base: Patient with Unique Clinical Moreover, Radiographic Presentation. Acta Med Iran. 53(1):69-73.
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