Case Report

Disseminated Juvenile Pilomyxoid Astrocytoma of the Hypothalamic-Chiasmatic Region

Abstract

Pilomyxoid astrocytoma (PMA) is a recently described histological type of pilocytic astrocytoma (PA), but the tumors show histological differences. PMA has more aggressive malignant behavior than PA. Magnetic Resonance Imaging (MRI) may play a crucial role in the preoperative setting and also help to establish an appropriate therapeutic regimen. In this case report, we illustrated MRI findings of a hypothalamic-chiasmatic PMA in a 15-year-old female patient presenting with extensive leptomeningeal seeding. The patient was operated for total tumor resection, but could not survive the second post-operative day. We have comprehensively discussed the clinical, imaging, and histopathological features of these relatively rare tumors and also reviewed the recent literature.

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Files
IssueVol 57, No 9 (2019) QRcode
SectionCase Report(s)
DOI https://doi.org/10.18502/acta.v57i9.2643
Keywords
Pilocytic astrocytoma Pilomyxoid astrocytoma Leptomeningeal Dissemination
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Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Mesrur Halefoglu A, Duran Ozel B. Disseminated Juvenile Pilomyxoid Astrocytoma of the Hypothalamic-Chiasmatic Region. Acta Med Iran. 2020;57(9):569-571.