Articles

Autoimmune Polyglandular Syndrome Type 2: An Unusual Presentation

Abstract

Autoimmune polyglandular syndrome (APS) type 2 is characterized by the presence of Addison's disease, in association with autoimmune thyroid disease and/or type 1 diabetes mellitus. APS type 2 occurs most often in middle aged females and is rare in children. Here an 11 year old boy is reported with Addison's disease who developed symptom's of diabetes mellitus, goiter, malabsorption, macrocytic anemia and keratitis. APS type 2 occurs most often in middle aged females and is quite rare in children but one should think to autoimmune poly glandular syndrome type II in patient at any age especially in patients with Addison's disease.

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IssueVol 48, No 3 (2010) QRcode
SectionArticles
Keywords
Polyendocrinopathies autoimmune Addison disease diabetes mellitus
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Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Karamifar H, Dalili S, Karamizadeh Z, Amirhakimi G, Dalili H. Autoimmune Polyglandular Syndrome Type 2: An Unusual Presentation. Acta Med Iran. 1;48(3):196-197.