Intra-Abdominal Desmoplastic Small Round Cell Tumor in A 45-Year-Old Man: A Case Report

  • Mandana Ashrafi Department of Pathology, Tehran University of Medical Sciences, Tehran, Iran.
  • Hiva Saffar Department of Pathology, Tehran University of Medical Sciences, Tehran, Iran.
  • Seyed Rasoul Mirsharifi Department of Pathology, Tehran University of Medical Sciences, Tehran, Iran.
  • Seyed Mohammad Tavangar Mail Department of Pathology, Tehran University of Medical Sciences, Tehran, Iran.
Keywords:
Adult, Desmoplastic small round cell tumor, Intra-abdominal

Abstract

Intra-abdominal desmoplastic small round cell tumor is a rare entity with a few reports worldwide. This tumor commonly occurs in children and adolescent and occurrence in adult age group is very rare. Here, we describe an adult male with symptoms of intestinal obstruction due to abdominal mass, located in splenic flexure. After resection, the diagnosis of intra-abdominal desmoplastic small round cell tumor was established by pathologic and immunohistochemical studies. We emphasize that albeit being rare, this tumor should be mentioned as one of the differential diagnoses of widespread intra-abdominal lesions in any age group.  A brief review of epidemiology, clinical manifestations as well as pathological and molecular features is also included in the paper.

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How to Cite
1.
Ashrafi M, Saffar H, Mirsharifi SR, Tavangar SM. Intra-Abdominal Desmoplastic Small Round Cell Tumor in A 45-Year-Old Man: A Case Report. Acta Med Iran. 51(8):583-586.
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